A rare neuroblastoma location in the pelvis
Abstract
Neuroblastoma is the most common extracranial solid malignant tumor in children that is most often located inthe abdomen (suprarenal gland, sympathetic chain) and mediastinum, while other locations are rare. The treatment is surgery, chemotherapy and radiotherapy. In this article we present a rare case of neuroblastoma originating from sacral plexus in a 9-month-old female infant, with infiltration of the obturator channel. We performed tumor extirpation with paraaortal and iliacal lymphadenectomy, while a small portion of the tumor remained in the obturator channel because the attempt of complete removal would carry a significant risk of nerve damage. Radical removal is not recommended because it carries a high risk of nerve damage without improving overall survival.
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References
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